Prune belly syndrome (PBS) is a congenital anomaly syndrome characterized by triad of abdominal musculature deficiency and malous development of the urinary tract and bilateral cryptorchidsm. The syndrome seems to be sporadic affecting predominantly boys Etiopathophysio logy of PBS remains unknown but may be caused by primary mesodermal development defect. PBS can be defect. PBS can be detecte…
Gagal ginjal kronik (GGK) ialah kehilangan fungsi ginjal progresif dan irevesbel mulai tahap ringan sampai gagal ginjal tahap akhir. Diagnosis dini GGK pada anak sering sulit ditegakkan karena presentasi klinis awal bervariasi dan tidak spesifik. Diagnosis dan pengobatan konservatif sejak awal penyakit dapat memperlambat progresifitas penyakit dan penggunaan pengobatan pengganti ginjal. Melacak…